FlashcardsMedical conditions: Craniofacial & dental genetics

Beckwith–Wiedemann syndrome flashcards

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How does Beckwith–Wiedemann syndrome affect dental management?

1 / 6

How does Beckwith–Wiedemann syndrome affect dental management?

Airway: Treat a large tongue as an airway finding: ask about obstructive breathing and difficult airway history
Tongue reduction: Partial glossectomy (tongue reduction) is planned with the craniofacial team for airway, feeding, speech or occlusion
Growth and relapse: Coordinate tongue surgery and orthodontics rather than assuming one operation will correct the bite.
Growth effect: Persistent macroglossia and growth can influence occlusion and relapse
Before anesthesia: Review hypoglycemia history before fasting for anesthesia; confirm tumor surveillance is current